Refractory coeliac disease associated with late onset epilepsy, ataxia, tremor and progressive myoclonus with giant cortical evoked potentials—A case report and review of literature
نویسندگان
چکیده
Population-based screening studies suggest an overall prevalence of coeliac disease in Western populations of about 1%. A variety of neurological problems have been associated with coeliac disease occurring in up to 10% of cases of adult coeliac disease. We report an interesting case of a patient with coeliac disease who subsequently developed neurological symptoms several years later. Furthermore, a literature review of all cases to date was performed.
منابع مشابه
[Recent advance in research of benign adult familial myoclonus epilepsy (BAFME): is BAFME a progressive disorder?].
Benign adult familial myoclonus epilepsy (BAFME) is an adult onset, autosomal dominant disease characterized by cortical tremor and infrequent generalized seizures. BAFME was considered as non-progressive, but cortical tremor worsened in some of the aged patients. We investigated the disease progression of BAFME. Cortical tremor significantly worsened and amplitudes of giant somatosensory evoke...
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عنوان ژورنال:
- Seizure
دوره 21 شماره
صفحات -
تاریخ انتشار 2012